Malignant Peripheral Nerve Sheath Tumour Arising From Solitary Sclerotic Neurofibroma.
نویسندگان
چکیده
Neurofibroma is a benign neoplasm of the peripheral nerve, which occurs as multiple tumours in neurofibromatosis type 1 (NF1) or as a solitary tumour with no association with NF1. Malignant change is sometimes reported in neurofibroma in NF1, but there are few reports of malignant transformation of solitary neurofibroma. We report here a case of malignant change in a solitary sclerotic neurofibroma following 3 recurrences.
منابع مشابه
Malignant peripheral nerve sheath tumour arising within neurofibroma. An immunohistochemical analysis in the comparison between benign and malignant components.
AIMS To compare the expression of immunohistochemical variables between benign and malignant components of malignant peripheral nerve sheath tumour (MPNST) arising within neurofibroma. METHODS Eight cases of MPNST arising within a neurofibroma, associated with neurofibromatosis type 1 (NF1), were studied. The areas of MPNST and neurofibroma were compared immunohistochemically with regard to t...
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ورودعنوان ژورنال:
- Acta dermato-venereologica
دوره 96 5 شماره
صفحات -
تاریخ انتشار 2016